Figure 4.

Effects of decreased β-oxidation and increased ω-oxidation of fatty acids and VPA on the urea cycle. See text for further details. NAGA, N-acetyl glutamic acid; CoA, coenzyme A; CPS, carbamyl phosphate synthetase; OTC, ornithine transcarbamylase; 4-en-VPA, 2-propyl-4-pentenoic acid.